摘要
目的 探讨阑尾神经内分泌肿瘤（appendiceal neuroendocrine tumor, aNET）的临床特点，并复习相关文献。方法 回顾分析2025年8月我院收治的1例阑尾炎术后偶然发现的儿童aNET临床资料。结果 患者女性，8岁，因腹痛1天入院。血常规示白细胞计数16.29×10⁹/L。结合腹部查体及CT检查，考虑急性阑尾炎，急诊行阑尾切除术。术后病理检查偶然发现为aNET，术中未行冰冻切片及淋巴结活检。结论 aNET是一类罕见的消化道肿瘤，常见于中老年女性，儿童病例极为罕见。在低龄儿童急性阑尾炎手术过程中，重视病理检查结果对避免漏诊具有重要意义。
关键词： 急性阑尾炎；阑尾肿瘤；神经内分泌肿瘤；儿童；鉴别诊断
Abstract
Objective To investigate the clinical characteristics of appendiceal neuroendocrine tumor (aNET) and review the relevant literature. Methods We retrospectively analyzed the clinical data of a pediatric case of aNET that was incidentally discovered after appendectomy in August 2025. Results An 8-year-old girl was admitted with a 1-day history of abdominal pain. Laboratory tests revealed a white blood cell count of 16.29×10⁹/L. Based on abdominal examination and CT findings, acute appendicitis was suspected, and emergency appendectomy was performed. Postoperative pathology unexpectedly confirmed aNET. No intraoperative frozen section or lymph node biopsy was performed. Conclusion s aNET is a rare gastrointestinal tumor, most commonly seen in middle-aged and elderly women, with pediatric cases being extremely uncommon. In young children undergoing surgery for acute appendicitis, careful pathological evaluation is crucial to avoid missed diagnosis.
Key words： Acute appendicitis; Appendiceal neoplasms; Neuroendocrine neoplasms; Child; Differential diagnosis
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